CHAPTER 6
REFERENCES
General Aspects
1. Alagille D, Odièvre M: Liver and Biliary Tract Disease in Children. New York, 1979, Wiley-Flammarion.
2. Balistreri WF: Medical progress: Neonatal cholestasis. J Pediatr 106; 171-184, 1985.
3. Balistreri WF: Neonatal cholestasis: Lessons from the past, issues for the future. Semin Liver Dis 7: 61-66, 1987.
4. Desmet VJ: Intrahepatic bile ducts under the lens. J Hepatology 1: 545-559, 1985.
5. Desmet VJ: Cholangiopathies: Past, present, and future. Semin Liver Dis 7: 67-76, 1987.
6. Ghishan FK, LaBrecque DR, Mitros FA, Younoszai MK: The evolving nature of "infantile obstructive cholangiopathy." J Pediatr 97: 27-32, 1980.
7. Haber BA, Lake AM: Cholestatic jaundice in the newborn. Clin Perinatol 17: 483-506, 1990.
8. Heubi JE, Daugherty CC: Neonatal cholestasis: An approach for the practicing pediatrician. Curr Prob Pediatr 20:235-295, 1990.
9. Landing BH: Considerations of the pathogenesis of neonatal hepatitis, biliary atresia and choledochal cyst -- The concept of infantile obstructive cholangiopathy. Prog Pediatr Surg 6: 113-139, 1974.
Biliary Atresia
10. Abramson SJ, Berdon WE, Altman RP, et al: Biliary atresia and noncardiac polysplenic syndrome: US and surgical considerations. Radiology 163: 377-379, 1987.
11. Adelman S: Prognosis of uncorrected biliary atresia: An update. J Pediatr Surg 13: 389-391, 1978.
12. Alagille D: Extrahepatic biliary atresia. Hepatology 4: 7S-10S, 1984.
13. Altman RP, Abramson S: Potential errors in the diagnosis and surgical management of neonatal jaundice. J Pediatr Surg 20: 529-534, 1985.
14. Andrews AS, Wanek E, Fyock B, et al: Pediatric liver transplantation: A 3-year experience. J Pediatr Surg 24: 77-82, 1989.
15. Balistreri WF, Bove KE: Hepatobiliary consequences of parenteral alimentation. Prog Liver Dis 9: 567-601, 1990.
16. Bill AH, Haas JE, Foster GL: Biliary atresia: Histopathologic observations and reflections upon its natural history. J Pediatr Surg 12: 977-982, 1977.
17. Brough AJ, Bernstein J: Conjugated hyperbilirubinemia in early infancy. Hum Pathol 5: 507-516, 1974.
18. Brown WR, Sokol RJ, Levin MJ, et al: Lack of correlation between infection with reovirus 3 and extrahepatic biliary atresia or neonatal hepatitis. J Pediatr 113: 670-676, 1988.
19. Chandra RS: Biliary atresia and other structural anomalies in the congential polysplenia syndrome. J Pediatr 85: 649-655, 1974.
20. Chandra RS: Bile duct and hepatic morphology in biliary atresia: Correlation with bile flow following portoenterostomy. In Daum F (ed): Extrahepatic Biliary Atresia. New York, 1983, Marcel Dekker Inc. pp 43-63.
21. Chandra RS, Altman RP: Ductal remnants in extrahepatic biliary atresia: A histopathologic study with clinical correlation. J Pediatr 93: 196-200, 1978.
22. Cunningham ML, Sybert VP: Idiopathic extrahepatic biliary atresia: Recurrence in sibs in two families. Am J Med Genet 31: 421-426, 1988.
23. Deguchi E, Yanagihara J, Iwai N: Bile duct patterns in the hilar region of the liver in two cases of biliary atresia. J Pediatr Surg 25: 307-310, 1990.
24. Dessanti A, Ohi R, Hanamatsu M, et al: Short term histological liver changes in extrahepatic biliary atresia with good postoperative bile drainage. Arch Dis Child 60: 739-742, 1985.
25. Esquivel CO, Iwatsuki S, Gordon RD, et al: Indications for pediatric liver transplantation. J Pediatr 111: 1039-1045, 1987.
26. Fain JS, Lewin KJ: Intrahepatic biliary cysts in congenital biliary atresia. Arch Pathol Lab Med 113: 1383-1386, 1989.
27. Ferry GD, Selby ML, Udall J, et al: Guide to early diagnosis of biliary obstruction in infancy. Review of 143 cases. Clin Pediatr 24: 305-311, 1985.
28. Gautier M, Eliot N: Extrahepatic biliary atresia. Morphological study of 98 biliary remnants. Arch Pathol Lab Med 105: 397-402, 1981.
29. Gautier M, Jehan P, Odièvre M: Histologic study of biliary fibrous remnants in 48 cases of extrahepatic biliary atresia: Correlation with postoperative bile flow restoration. J Pediatr 89: 704-709, 1976.
30. Gautier M, Moitier G, Odièvre M: "Uncorrectable" extrahepatic biliary atresia: Relationship between intrahepatic bile duct pattern and surgery. J Pediatr Surg 15: 129-132, 1980.
31. Gautier M, Valayer J, Odièvre M, Alagille D: Histological liver evaluation 5 years after surgery for extrahepatic biliary atresia: A study of 20 cases. J Pediatr Surg 19: 263-268, 1984.
32. Gershoni-Baruch R, Gottfried E, Pery M, et al: Immotile cilia syndrome including polysplenia, situs inversus, and extrahepatic biliary atresia. Am J Med Genet 33: 390-393, 1989.
33. Glaser JH, Morecki R: Reovirus type 3 and neonatal cholestasis. Semin Liver Dis 7: 100-107, 1987.
34. Grosfeld JL, Fitzgerald JF, Predaina R, et al: The efficacy of hepatoportoenterostomy in biliary atresia. Surgery 106: 692-701, 1989.
35. Haas JE: Bile duct and liver pathology in biliary atresia. World J Surg 2: 561-569, 1978.
36. Hadchouel M, Gautier M, Valayer J, et al: Histopathology of the liver five years after successful surgery for extrahepatic biliary atresia. In Daum F (ed): Extrahepatic biliary atresia. New York, 1983, Marcel Dekker Inc. pp 65-70.
37. Hadchouel M, Hogan RN, Odièvre M: Immunoglobulin deposits in the biliary remnants of extrahepatic biliary atresia: a study by immunoperoxidase staining in 128 infants. Histopathology 5: 217-221,1981.
38. Hart MH, Kaufman SS, Vanderhoof JA, et al: Neonatal hepatitis and extrahepatic biliary atresia associated with cytomegalovirus infection in twins. Am J Dis Child 145: 302-305, 1991.
39. Hashimoto T, Yura J: Percutaneous transhepatic cholangiography (PTC) in biliary atresia with special reference to the structure of the intrahepatic bile ducts. J Pediatr Surg 16: 22-25, 1981.
40. Hays DM, Kimura K: Biliary atresia: New concepts of management. Curr Prob Surg 18: 546-608, 1981.
41. Houwen RHJ, Zwierstra RP, Severijnen RSVM, et al: Prognosis of extrahepatic biliary atresia. Arch Dis Child 64: 214-218, 1989.
42. Howard ER: Extrahepatic biliary atresia: a review of current management. Br J Surg 70: 193-197, 1983.
43. Ito T, Horisawa M, Ando H: Intrahepatic bile ducts in biliary atresia -- A possible factor determining the prognosis. J Pediatr Surg 18: 124-130, 1983.
44. Karrer FM, Lilly JR, Stewart BA, Hall RJ: Biliary atresia registry, 1976 to 1989. J Pediatr Surg 25: 1076-1081, 1990.
45. Kasai M: Treatment of biliary atresia with special reference to hepatic porto-enterostomy and its modifications. Prog Pediatr Surg 6: 552, 1974.
46. Landing BH, Wells TR, Ramicone E: Time course of the intrahepatic lesion of extrahepatic biliary atresia. A morphometric study. Pediatr Pathol 4: 309-319, 1985.
47. Laurent J, Gauthier F, Bernard O, et al: Long-term outcome after surgery for biliary atresia. Study of 40 patients surviving for more than 10 years. Gastroenterology 99: 1793-1797, 1990.
48. Lawrence D, Howard ER, Tzannatos C, Mowat AP: Hepatic portoenterostomy for biliary atresia. A comparative study of histology and prognosis after surgery. Arch Dis Child 56: 460-463, 1981.
49. Lilly JR, Hall RJ, Vasquez-Estevez J, et al: The surgery of "correctable" biliary atresia. J Pediatr Surg 22: 522-525, 1987.
50. Lilly JR, Karrer KM, Hall RJ, et al: The surgery of biliary atresia. Ann Surg 210: 289-294, 1989.
51. Lurie M, Elmalach I, Schuger L, Weintraub Z: Liver findings in infantile cytomegalovirus infection: similarity to extrahepatic biliary obstruction. Histopathology 11: 1171-1180, 1987
52. Maksem JA: Polysplenia syndrome and splenic hypoplasia associated with extrahepatic biliary atresia. Arch Pathol Lab Med 104: 212-214, 1980.
53. Manolaki AG, Larcher VF, Mowat AP, et al: The prelaparotomy diagnosis of extrahepatic biliary atresia. Arch Dis Child 58: 591-594, 1983.
54. McDonald PJ, Stehman FB, Stewart DR: Infantile obstructive cholangiopathy. Am J Dis Child 133: 518-522, 1979.
55. Mieli-Vergani G, Howard ER, Portman B, Mowat AP: Late referral for biliary atresia -- missed opportunities for effective surgery. Lancet 1: 421-423, 1989.
56. Miyano T, Suruga K, Tsuchiya H, Suda K: A histopathological study of the remnant of extrahepatic bile duct in so-called uncorrectable biliary atresia. J Pediatr Surg 12: 19-25, 1977.
57. Miyano T, Suruga K, Suda K: Abnormal choledocho-pancreatico ductal junction related to etiology of infantile obstructive jaundice diseases. J Pediatr Surg 14: 16 ,1979.
58. Morecki R, Glaser JH, Cho S, et al: Biliary atresia and reovirus type 3 infection. N Engl J Med 307: 481-484, 1982.
59. Mowat AP: Biliary disorders in childhood. Semin Liver Dis 2: 271-281, 1982.
60. Mowat AP, Psacharopoulos HT, Williams R: Extrahepatic biliary atresia versus neonatal hepatitis. Review of 137 prospectively investigated infants. Arch Dis Child 51: 763-770, 1976.
61. Nord KS, Saad S, Joshi VV, McLoughlin LC: Concurrence of alpha-1-antitrypsin deficiency and biliary atresia. J Pediatr 111: 416-418, 1987.
62. Ohi R, Lilly JR: Copper kinetics in infantile hepatobiliary disease. J Pediatr Surg 15: 509-512, 1980.
63. Ohi R, Shikes RH, Stellin GP, Lilly JR: In biliary atresia duct histology correlates with bile flow. J Pediatr Surg 19: 467-470, 1984.
64. Ohuchi N, Ohi R, Takahashi T, Kasai M: Postoperative changes of intrahepatic portal veins in biliary atresia -- A 3-D reconstruction study. J Pediatr Surg 21: 10-14, 1986.
65. Psacharopoulos HT, Howard ER, Portmann B, Mowat AP: Extrahepatic biliary atresia: properative assessment and surgical results in 47 consecutive cases. Arch Dis Child 55: 851-856, 1980.
66. Raweily EA, Gibson AAM, Burt AD: Abnormalities of intrahepatic bile ducts in extrahepatic biliary atresia. Histopathology 17: 521-527, 1990.
67. Ryckman FC, Noseworthy J: Neonatal cholestatic conditions requiring surgical reconstruction. Semin Liver Dis 7: 134-154, 1987.
68. Schwartz MZ, Hall RJ, Reubner B, et al: Agenesis of the extrahepatic bile ducts: Report of five cases. J Pediatr Surg 25: 805-807, 1990.
69. Stewart BA, Hall RJ, Lilly JR: Liver transplantation and the Kasai operation in biliary atresia. J Pediatr Surg 23: 623-626, 1988.
70. Suruga K, Miyano T, Arai T, et al: A study of patients with long term bile flow after hepatic portoenterostomy for biliary atresia. J Pediatr Surg 20: 252-255, 1985.
71. Teichberg S, Markowitz J, Silverberg M, et al: Abnormal cilia in a child with the polysplenia syndrome and extrahepatic biliary atresia. J Pediatr 100: 399-401, 1982.
72. Tolaymat N, Figueroa-Colon R, Mitros FA:
73. Vazquez-Estevez J, Stewart B, Shikes RH, et al: Biliary atresia: Early determination of prognosis. J Pediatr Surg 24: 48-51, 1989.
74. Weinberg AG, Finegold MJ: Primary hepatic tumors of childhood. Hum Pathol 14: 512-537, 1983.
75. Wilkinson ML, Mieli-Vergani G, Ball C, et al: Endoscopic retrograde cholangiopancreatography in infantile cholestasis. Arch Dis Child 66: 121-123, 1991.
76. Witzleben CL: Extrahepatic biliary atresia: Concepts of cause, diagnosis, and management. Persp Pediatr Pathol 5: 41-62, 1979.
77. Witzleben CL, Buck BE, Schnaufer L, Brzosko WJ: Studies on the pathogenesis of biliary atresia. Lab Invest 38: 525-532, 1978.
78. Wood RP, Langnas AN, Stratta RJ, et al: Optimal therapy for patients with biliary atresia: Portoenterostomy ("Kasai" procedures) versus primary transplantation. J Pediatr Surg 25: 153-162, 1990.
Other Causes of Biliary Obstruction
79. Chapoy PR, Kendall RS, Fonkalsrud E, Ament ME: Congential stricture of the common hepatic duct: An unusual case without jaundice. Gastroenterology 80: 380-383, 1981.
80. Cheney M, Gustad DG, Lilly JR: Choledochal cyst. World J Surg 9: 244-249, 1985.
81. Descos B, Bernard O, Brunelle F, et al: Pigment gallstones of the common bile duct in infancy. Hepatology 4: 678-683, 1984.
82. Holcomb GW Jr, O'Neill JA Jr, Holcomb GW III: Cholecystitis, cholelithiasis and common duct stenosis in children and adolescents. Ann Surg 191: 626-634, 1980.
83. Howard ER, Johnston DI, Mowat AP: Spontaneous perforation of common bile duct in infants. Arch Dis Child 51: 883-886, 1976.
84. Howell CG, Templeton JM, Weiner S, et al: Antenatal diagnosis and early surgery for choledochal cyst. J Pediatr Surg 18: 387-393, 1983.
85. Lack EE, Perez-Atayde AR, Schuster SR: Botryoid rhabdomyosarcoma of the biliary tract. Report of five cases with ultrastructural observations and literature review. Am J Surg Pathol 5: 643-652, 1981.
86. O'Neill JA Jr, Templeton JM Jr, Schnauffer L, et al: Recent experience with choledochal cyst. Ann Surg 205: 533-539, 1987.
87. Ruymann FB, Raney RB Jr, Crist WM, et al: Rhabdomyosarcoma of the biliary tree in childhood. A report from the intergroup rhabdomyosarcoma study. Cancer 56: 575-581, 1985.
88. Sokal EM, de Goyet J de V, Buts JP, et al: Unifocal stricture of the common bile duct in two children: A localized form of primary sclerosing cholangitis. J Pediatr Gastroenterol Nutr 11: 268-274, 1990.
89. Stringel G, Mercer S: Idiopathic perforation of the biliary tract in infancy. J Pediatr Surg 18: 546-550, 1983.
Neonatal Hepatitis
90. Alagille D: Cholestasis in the first three months of life. Prog Liver Dis 6: 471-485, 1979.
91. Bosman C, Baldini D, Boldrini R, et al: Aplastic anemia and neonatal giant-cell hepatitis. Appl Pathol 6: 49-55, 1988.
92. Chang MH, Hsu HC, Lee CY, et al: Neonatal hepatitis: A follow-up study. J Pediatr Gastroenterol Nutr 6: 203-207, 1987.
93. Clayton PT, Leonard JV, Lawson AM, et al: Familial giant cell hepatitis associated with synthesis of 3β,7α-dihydroxy- and 3β,7α,12α-trihydroxy-5-cholenoic acids. J Clin Invest 79: 1021-1038, 1987.
94. Craig JM, Landing BH: Form of hepatitis in neonatal period simulating biliary atresia. Arch Pathol 54: 321-333, 1952.
95. Danks DM, Campbell PE, Jack I, et al: Studies of the aetiology of neonatal hepatitis and biliary atresia. Arch Dis Child 52: 360-367, 1977.
96. Deutsch J, Smith AL, Danks DM, Campbell PE: Long term prognosis for babies with neonatal liver disease. Arch Dis Child 60: 447-451, 1985.
97. Dick MC, Mowat AP: Hepatitis syndrome in infancy -- an epidemiological survey with 10 year follow up. Arch Dis Child 60: 512-516, 1985.
98. Heathcote J, Deodhar KP, Scheuer PJ, Sherlock S: Intrahepatic cholestasis in childhood. N Engl J Med 295: 801-805, 1976.
99. Henriksen NT, Drabløs P-A, Aagenaes Ø: Cholestatic jaundice in infancy. The importance of familial and genetic factors in aetiology and prognosis. Arch Dis Child 56: 622-627, 1981.
100. Herman SP, Baggenstoss AH, Cloutier MD: Liver dysfunction and histologic abnormalities in neonatal hypopituitarism. J Pediatr 87: 892-895, 1975.
101. Kaufman FR, Costin G, Thomas DW: Neonatal cholestasis and hypopituitarism. Arch Dis Child 59: 787-789, 1984.
102. Montgomery CK, Ruebner BH: Neonatal hepatocellular giant cell transformation: A review. Perspect Pediatr Pathol 3: 85-101, 1976.
103. Odièvre M, Hadchouel M, Landrieu P, et al: Long-term prognosis for infants with intrahepatic cholestasis and patent extrahepatic biliary tract. Arch Dis Child 56: 373-376, 1981.
104. Pessayre D, Degos F, Feldmann G, et al: Chronic active hepatitis and giant multinucleated hepatocytes in adults treated with clometacin. Digestion 22: 66-72, 1981.
105. Phillips MJ, Blendis LM, Poucell S, et al: Syncytial giant-cell hepatitis. Sporadic hepatitis with distinctive pathological features, a severe clinical course, and paramyxoviral features. N Engl J Med 324: 455-460, 1991.
106. Richey J, Rogers S, Van Thiel DH, Lester R: Giant multinucleated hepatocytes in an adult with chronic active hepatitis. Gastroenterology 73: 570-574, 1977.
107. Ruebner BH, Miyai K: The pathology of neonatal hepatitis and biliary atresia with particular reference to hematopoiesis and hemosiderin deposition. Ann NY Acad Sci 111: 375-391, 1963.
108. Ruebner BH, Thaler MM: Giant-cell transformation in infantile liver disease. In Javitt N (ed): Neonatal hepatitis and biliary atresia. Washington DC, 1979, NIH DHEW. pp 167-171.
109. Semeraro LA, Riely CA, Kolodny EH, et al: Niemann-Pick variant lipidosis presenting as "neonatal hepatitis". J Pediatr Gastroenterol Nutr 5: 492-500, 1986.
110. Setchell KDR, Suchy FJ, Welsh MB, et al: Δ4-3-oxosteroid 5β-reductase deficiency described in identical twins with neonatal hepatitis. A new inborn error in bile acid synthesis. J Clin Invest 82: 2148-2157, 1988.
111. Shah MC, Barton LL: Congenital syphilitic hepatitis. Pediatr Infect Dis J 8: 891-892, 1989.
112. Spichtin HP, Gudat F, Schmid M, et al: Microtubular aggregates in human chronic non-A, non-B hepatitis with bridging hepatic necrosis and multinucleated giant cells. Liver 2: 355-360, 1982.
113. Thaler H: Post-infantile giant cell hepatitis. Liver 2: 393-403, 1982.
114. Thijs JC, Bosma A, Henzen-Logmans SC, Meuwissen SGM: Postinfantile giant cell hepatitis in a patient with multiple autoimmune features. Am J Gastroenterol 80: 294-297, 1985.
115. Witzleben CL, Marshall GS, Wenner W, et al: HIV as a cause of giant cell hepatitis. Hum Pathol 19: 603-605, 1988.
Paucity of Interlobular Bile Ducts
116. Adams PC: Hepatocellular carcinoma associated with arteriohepatic dysplasia. Dig Dis Sci 31: 438-442, 1986.
117. Alagille D, Estrada A, Hadchouel M, et al: Syndromic paucity of interlobular bile ducts (Alagille syndrome or arteriohepatic dysplasia): Review of 80 cases. J Pediatr 110: 195-200, 1987.
118. Alagille D, Odievre M, Gautier M, Dommergues JP: Hepatic ductular hypoplasia associated with characteristic facies, vertebral malformations, retarded physical, mental, and sexual development, and cardiac murmur. J Pediatr 86: 63-71, 1975.
119. Berman MD, Ishak KG, Schaefer EJ, et al: Syndromatic hepatic ductular hypoplasia (arteriohepatic dysplasia). A clinical and hepatic histologic study of three patients. Dig Dis Sci 26: 485-497, 1981.
120. Branski D, Lebenthal E, Hatch TF, et al: Intrahepatic cholestasis for 15 years without cirrhosis. J Clin Gastroenterol 2: 251-257, 1980.
121. Byrne JL, Harrod MJ, Friedman JM, Howard-Peebles PN: del(20p) with manifestations of arteriohepatic dysplasia. Am J Med Genet 24: 673-678, 1986.
122. Dahms BB, Petrelli M, Wyllie R, et al: Arteriohepatic dysplasia in infancy and childhood: A longitudinal study of six patients. Hepatology 2: 350-358, 1982.
123. Deprettere A, Portmann B, Mowat AP: Syndromic paucity of intrahepatic bile ducts: Diagnostic difficulty; severe morbidity throughout early childhood. J Pediatr Gastroenterol Nutr 6: 865-871, 1987.
124. Eyssen H, Eggermont E, Van Eldere J, et al: Bile acid abnormalities and the diagnosis of cerebro-hepato-renal syndrome (Zellweger syndrome). Acta Pædiatr Scand 74: 539-544, 1985.
125. Finegold MJ, Carpenter RJ: Obliterative cholangitis due to cytomegalovirus: A possible precursor of paucity of intrahepatic bile ducts. Hum Pathol 13: 662-665, 1982.
126. Gorelick FS, Dobbins JW, Burrell M, Riely CA: Biliary tract abnormalities in patients with arteriohepatic dysplasia. Dig Dis Sci 27: 815-820, 1982.
127. Hadchouel M, Hugon RN, Gautier M: Reduced ratio of portal tracts to paucity of intrahepatic bile ducts. Arch Pathol Lab Med 102: 402, 1978.
128. Hanson RF, Isenberg JN, Williams GC, et al: The metabolism of 3α, 7α, 12α-trihydroxy-5β-cholestan-26-oic acid in two siblings with cholestasis due to intrahepatic bile duct anomalies. An apparent inborn error of cholic acid synthesis. J Clin Invest 56: 577-587, 1975.
129. Hashida Y, Yunis EJ: Syndromatic paucity of interlobular bile ducts: Hepatic histopathology of the early and endstage liver. Pediatr Pathol 8: 1-15, 1988.
130. Kahn EI, Daum F, Markowitz J, et al: Arteriohepatic dysplasia. II. Hepatobiliary morphology. Hepatology 3: 77-84, 1983.
131. Kahn E, Daum F, Markowitz J, et al: Nonsyndromatic paucity of interlobular bile ducts: Light and electron microscopic evaluation of sequential liver biopsies in early childhood. Hepatology 6: 890-901, 1986.
132. Kahn E, Markowitz J, Aiges H, Daum F: Human ontogeny of the bile duct to portal space ratio. Hepatology 10: 21-23, 1989.
133. Kaufman SS, Wood RP, Shaw BW Jr, et al: Hepatocarcinoma in a child with the Alagille syndrome. Am J Dis Child 141: 698-700, 1987.
134. Kocoshis SA, Cottrill CM, O'Connor WN, et al: Congential heart diseae, butterfly vertebrae, and extrahepatic biliary atresia: A variant of arteriohepatic dysplasia. J Pediatr 99: 436-439, 1981.
135. LaBrecque DR, Mitros FA, Nathan RJ, et al: Four generations of arteriohepatic dysplasia. Hepatology 2: 467-474, 1982.
136. Markowitz J, Daum F, Kahn EI, et al: Arteriohepatic dysplasia. I. Pitfalls in diagnosis and management. Hepatology 3: 74-76, 1983.
137. Mueller RF. The Alagille syndrome (arteriohepatic dysplasia). J Med Genet 24: 621-626, 1987.
138. Mueller RF, Pagon RA, Pepin MG, et al: Arteriohepatic dysplasia: phenotypic features and family studies. Clin Genet 25: 323-331, 1984.
139. Novotny NM, Zetterman RK, Antonson DL, Vanderhoof JA: Variation in liver histology in Alagille's syndrome. Am J Gastroenterol 75: 449-450, 1981.
140. Perrault J: Paucity of interlobular bile ducts. Getting to know it better. Dig Dis Sci 26: 481-484, 1981.
141. Rabinovitz M, Imperial JC, Schade RR, Van Thiel DH: Hepatocellular carcinoma in Alagille's syndrome: A family study. J Pediatr Gastroenterol Nutr 8: 26-30, 1989.
142. Riely CA: Familial intrahepatic cholestatic syndromes. Semin Liver Dis 7: 119-133, 1987.
143. Riely CA, Cotlier E, Jensen PS, Klatskin G: Arteriohepatic dysplasia: A benign syndrome of intrahepatic cholestasis with multiple organ involvement. Ann Intern Med 91: 520-527, 1979.
144. Setchell KDR, Street JM: Inborn errors of bile acid synthesis. Semin Liver Dis 7: 85-99, 1987.
145. Shulman SA, Hyams JS, Gunta R, et al: Arteriohepatic dysplasia (Alagille syndrome): Extreme variability among affected family members. Am J Med Genet 19: 325-332, 1984.
146. Sokol RJ, Heubi JE, Balistreri WF: Intrahepatic "cholestatic facies": Is it specific for Alagille syndrome? J Pediatr 103: 205-208, 1983.
147. Valencia-Mayoral P, Weber J, Cutz E, et al: Possible defect in the bile secretory apparatus in arteriohepatic dysplasia (Alagille's syndrome): A review with observations on the ultrastructure of liver. Hepatology 4: 691-698, 1984.
148. Watson GH, Miller V: Arteriohepatic dysplasia. Familial pulmonary arterial stenosis with neonatal liver disease. Arch Dis Child 48: 459-466, 1973.
149. Witzleben CL: Bile duct paucity ("intrahepatic atresia"). Perspect Pediatr Pathol 7: 185-201, 1982.
150. Witzleben CL, Finegold M, Piccoli DA, Treem WR: Bile canalicular morphometry in arteriohepatic dysplasia. Hepatology 7: 1262-1266, 1987.
151. Zhang F, Deleuze J-F, Aurias A, et al: Interstitial deletion of the short arm of chromosome 20 in arteriohepatic dysplasia (Alagille syndrome). J Pediatr 116: 73-77, 1990.
PROGRESSIVE FAMILIAL CHOLESTASIS OF CHILDHOOD
152. Aagenæs Ø: Hereditary recurrent cholestasis with lymphoedema -- two new families. Acta Pædiatr Scand 63: 465-471, 1974.
153. Aagenæs Ø, Van der Hagen CB, Refsum S: Hereditary recurrent intrahepatic cholestasis from birth. Arch Dis Child 43: 646-657, 1968.
154. Ballow M, Margolis CA, Schachtel B, Hsia YE: Progressive familial intrahepatic cholestasis. J Pediatr 51: 998-1007, 1973.
155. Chobert MN, Bernard O, Bulle F, et al: High hepatic γ-glutamyltransferase (γ-GT) activity with normal serum γ-GT in children with progressive idiopathic cholestasis. J Hepatol 8: 22-25, 1989.
156. Clayton RJ, Iber FL, Ruebner BH, McKusick VA: Byler's disease: Fatal familial intrahepatic cholestasis in an Amish kindred. J Pediatr 67: 1025-1028, 1965.
157. Clayton RJ, Iber FL, Ruebner BH, McKusick VA: Byler disease. Fatal familial intrahepatic cholestasis in an Amish kindred. Amer J Dis Child 117: 112-124, 1969.
158. Dahms BB: Hepatoma in familial cholestatic cirrhosis of childhood. Its occurrence in twin brothers. Arch Pathol Lab Med 103: 30-33, 1979.
159. De Vos R, De Wolf-Peeters C, Desmet V, et al: Progressive intrahepatic cholestasis (Byler's disease): case report. Gut 16: 943-950, 1975.
160. Gray OP, Saunders RA: Familial intrahepatic cholestaic jaundice in infancy. Arch Dis Child 41: 320-328, 1966.
161. Jones EA, Rabin L, Buckley CH, et al: Progressive intrahepatic cholestasis of infancy and childhood. A clinicopathological study of a patient surviving to the age of 18 years. Gastroenterology 71: 675-682, 1976.
162. Odièvre M, Gautier M, Hadchouel M, Alagille D: Severe familial intrahepatic cholestasis. Arch Dis Child 48: 806-812, 1973.
163. Ornvold K, Nielsen I-M, Poulsen H: Fatal familial cholestatic syndrome in Greenland Eskimo children. A histomorphological analysis of 16 cases. Virchows Archiv A Pathol Anat 415: 275-281, 1989.
164. Ugarte N, Gonzalez-Crussi F: Hepatoma in sibling with progressive familial cholestatic cirrhosis of childhood. Am J Clin Pathol 76: 172-177, 1981.
165. Weber AM, Tuchweber B, Yousef I, et al: Severe familial cholestasis in North American Indian children: A clinical model of microfilament dysfunction? Gastroenterology 81: 653-662, 1981.
166. Whitington PF, Whitington GL: Partial external diversion of bile for the treatment of intractable pruritus associated with intrahepatic cholestasis. Gastroenterology 95: 130-136, 1988.
OTHER CHOLESTATIC DISORDERS
167. Alagille D: α-1-antitrypsin deficiency. Hepatology 4: 11S-14S, 1984.
168. Applebaum MN, Thaler MM: Reversibility of extensive liver damage in galactosemia. Gastroenterology 69: 496-502, 1975.
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