athologic Diagnosis

Final Clinico Pathologic Diagnosis

Description DX Code Body System
Biliary
Alagille Syndrome, Kasai ALLSYNK Hepatic
Alagille Syndrome, No Kasai ALLSYNO Hepatic
Alagille Syndrome, Unknown ALLSYNUNK Hepatic
Biliary Atresia, Unclassified BAUNK Hepatic
Secondary Biliary Cirrhosis, Iatrogenic BC2IAT Hepatic
Secondary Biliary Cirrhosis, Other, Specify BC2OTH Hepatic
Secondary Biliary Cirrhosis, Trauma BC2TRA Hepatic
Biliary Complications, Unspecified BICOMPUNS Hepatic
Biliary Hypoplasia, Kasai BIHYPOK Hepatic
Biliary Hypoplasia, No Kasai BIHYPOO Hepatic
Biliary Hypoplasia, Unknown BIHYPOUNK Hepatic
Caroli's Syndrome CAROLISYND Hepatic
Extra and Intra-Hepatic Biliary Atresia, Kasai EIBAK Hepatic
Extra and Intra-Hepatic Biliary Atresia, No Kasai EIBAO Hepatic
Extra and Intra-hepatic Biliary Atresia, Unknown EIBAUNK Hepatic
Extra-Hepatic Biliary Atresia, Kasai EXBAK Hepatic
Extra-Hepatic Biliary Atresia, No Kasai EXBAO Hepatic
Extra-Hepatic Biliary Atresia, Unknown EXBAUNK Hepatic
Intra-Hepatic Biliary Atresia, Kasai INBAK Hepatic
Intra-Hepatic Biliary Atresia, No Kasai INBAO Hepatic
Intra-Hepatic Biliary Atresia, Unknown INBAUNK Hepatic
Primary Biliary Cirrhosis PBC Hepatic
Primary Sclerosing Cholangitis, Crohn's disease PSCCRH Hepatic
Primary Sclerosing Cholangitis, No bowel Disease PSCNO Hepatic
Primary Sclerosing Cholangitis, Ulcerative Colitis PSCUC Hepatic
Primary Sclerosing Cholangitis, Unknown Bowel Disease PSCUNK Hepatic
Sclerosing Cholangistis, S/P Langerhans Cell Disease SCLCD Hepatic
Chronic GN 
Chronic GN CGN Not Specified
Cirrhotic GN CIRRGN Not Specified
Diffuse Proliferative GN (Rap Progr, Acute, Crescentic) DPROLGN Not Specified
Focal Proliferative GN (Focal GN) FPROLGN Not Specified
Heroin Induced GN HEROINGN Not Specified
Mesangio-Proliferative GN MESPROLGN Not Specified
Membranous GN MGN Not Specified
Membranoprolif GN (Mesangcap, Chrhypocompl, LOB, MixMemb) MPGN Not Specified
Post-Infectious GN (Acute Bacterial/Viral GN) POSTINFGN Not Specified
Post-Staphylococcal GN PSTAPHGN Not Specified
Post-Streptococcal GN PSTREPGN Not Specified
Post-Viral GN PVIRALGN Not Specified
Rapidly Progressive GN (RPGN) RPGN Not Specified
Chronic Hepatitis/Cirrhosis 
Autoimmune-Induced Cirrhosis CAHAI Hepatic
HBV-Induced Cirrhosis CAHB Hepatic
HBV+ Delta-Induced Cirrhosis CAHBD Hepatic
HCV-Induced Cirrhosis CAHC Hepatic
Drug-Induced Cirrhosis, Specify CAHDRUG Hepatic
Giant Cell Hepatitis CAHGC Hepatic
Non-A, Non-B CAH (Pre-1991 Cases) CAHNANB Hepatic
Neonatal Hepatitis, Chronic CAHNEO Hepatic
Chronic Hepatitis/Cirrhosis, Other, Specify CAHOTH Hepatic
Chronic Hepatitis/Cirrhosis, Unknown CAHUNK Hepatic
Cryptogenic Cirrhosis CCRYPT Hepatic
Developmental 
Caroli's Disease CAROLIS Hepatic
Congenital Hepatic Fibrosis CHF Hepatic
Choledochal Cyst CHOLCYST Hepatic
Polycystic Disease, NOS PCDNOS Unspecified
Polycystic Disease, Without Renal Involvment PCLD Unspecified
Polycystic Disease, With Renal Involvment PCLKD Unspecified
Diabetes 
Diabetes Nephropathy DM Not Specified
Drug Toxicity 
Cyclosporine Nephrotoxicity CYCLOTOX Not Specified
FK506 Toxicity FKTOX Not Specified
Toxins TOXINS Not Specified
FSGS/HUS/MPGN 
FSGS FSGS Not Specified
Focal-Segmental GS, Collapsing Variety FSGSCV Not Specified
Hemolytic-Uremic Syndrome HUS Not Specified
Type I (Subendothelial Deposits) Membranoprolif GN MPGNI Not Specified
Type II (Dense-Deposit Disease) Membranoprolif GN MPGNII Not Specified
Thrombocytopenic Purpura TTP Not Specified
Hypertension 
Hypertension HTN Not Specified
Malignant Hypertension MALIGHTN Not Specified
Renal Artery Stenosis RAS Not Specified
Infection, w/o Submassive Necrosis 
Adenovirus Infection INADV All
Bacterial Sepsis/Ischemia INBACSEP All
Cytomegalovirus, CMV Infection INCMV All
Enterovirus Infection INENV All
Influenza INFLUENZA Unspecified
Infection, Other, Specify INFOTH All
Fungal Sepsis INFUNGSEP All
Hepatitis B Virus INHBV Hepatic
Hepatitis B + Delta Virus INHBVD Hepatic
Hepatitis C Virus INHCV Hepatic
HHV VI Infection INHHVVI All
HHV VIII Infection INHHVVIII All
Human Immunodeficiency Virus, HIV INHIV All
Herpes Simplex Virus, Type I INHSV1 All
Herpes Simplex Virus, Unknown INHSVUNK All
Neonatal Hepatitis, Acute INNEO Hepatic
Papillomavirus INPAPV All
Herpes Simplex Virus, Type II INSHV2 All
Toxoplasmosis INTOXO All
Viral Sepsis INVIRALSEP All
Viral Infection, Other, Specify VIRALOTH Unspecified
Metabolic 
Alpha-1-Antitrypsin Deficiency A1ATD Hepatic
Amyloidosis, Primary AMY1 Hepatic
Amyloidosis, Secondary AMY2 Hepatic
Amyloidosis, FAP AMYFAP Hepatic
Amyloidosis, Other AMYOTH Hepatic
Amyloidosis, Unknown AMYUNK Hepatic
Cystic Fibrosis CF Hepatic
Familial Cholestasis, Byler FCBYLER Hepatic
Familial Cholestasis, Other FCOTH Hepatic
Familial Cholestasis, Summerskill FCSUMMER Hepatic
Fructosemia FRUCT Hepatic
Galactosemia GALAC Hepatic
Gaucher's Disease GAUCHER Hepatic
Glycogen Storage Disease, Type I GSDI Hepatic
Glycogen Storage Disease, Type IV GSDIV Hepatic
Hemochromatosis HEMOHO Hepatic
Hyperlipidemia, Type II HYLIP Hepatic
Indian Childhood Cirrhosis INDIANCC Hepatic
Metabolic Disease, Other, Specify METOTH All
Protein C Deficiency METPROC Unspecified
Neonatal Hemochromatosis NEOHEM Unspecified
Neurovisceral Storage Disease NEUVIS Unspecified
Niemann-Pick Disease NIEMPICK Unspecified
Porphyria, Protoporphyria PROTOPHY Unspecified
Reye's Syndrome REYES Unspecified
Tyrosinemia TYRO Unspecified
Wilson's Disease WILSON Unspecified
Wolman Disease WOLMAN Unspecified
Zellweger Syndrome ZELLWEGER Unspecified
Neoplasia 
Hepatic Adenoma(s) BNADEN Hepatic
Focal Nodular Hyperplasia(s) BNFNH Hepatic
Hemangioma BNHEM Hepatic
Lymphangiomyomatosis BNLYMGIO Hepatic
Mesenchymal Hamartoma BNMESHAM Hepatic
Nodular Regenerative Hyperplasia, NRH BNNRH Hepatic
Benign Neoplasia, Other, Specify BNOTH Hepatic
Inflammatory Pseudo-Tumor BNPSEU Hepatic
Vascular Malformation BNVASMAL Hepatic
Recurrent Malignancy DISRECM All
Metastatic Carcinoid MMCAR Unspecified
Erythrophagocytic Lymphohistiocytosis MMERYLYM Unspecified
Metastatic Gastrinoma MMGAS Unspecified
Germ Cell Tumor MMGCT Unspecified
Metastatic Glucagonoma MMGLU Unspecified
Metastatic Insulinoma MMINS Unspecified
Langerhans Cell Histiocytosis MMLCH Unspecified
Malignant Lymphoma, Non-PTLD MMLYM Unspecified
Lymphoma, Burkitt MMLYMBUR Unspecified
Lymphoma, HD MMLYMHD Unspecified
Lymphoma, Other MMLYMOTH Unspecified
Metastatic Neuroendocrine, NOS MMNEUENNOS Unspecified
Neuroblastoma MMNEURO Unspecified
Metastatic Malignancy, Other, Specify MMOTH Unspecified
Secondary Rhabdomyosarcoma MMRHABDO Unspecified
Spindle-Cell Tumor MMSCT Unspecified
Smooth Muscle Tumor MMSMT Unspecified
Teratoma MMTERAT Unspecified
Angiosarcoma MNANGIO Hepatic
Bile Duct Cancer, Without PSC MNBDCAO Hepatic
Bile Duct Cancer, With PSC MNBDCAP Hepatic
Mixed HCC/CC MNCCHCC Hepatic
Cholangiocarcinoma, NOS MNCCNOS Hepatic
Cholangiocarcinoma, Without PSC MNCCO Hepatic
Cholangiocarcinoma, With PSC MNCCP Hepatic
Epithelioid Hemangioendothelioma MNEH Hepatic
Hepatocellular Carcinoma, Fibrolamellar Variant MNFLHCC Hepatic
Hepatocellular Carcinoma, Normal Variant MNHCC Hepatic
Hepatoblastoma MNHPBLT Hepatic
Mesenchymal Sarcoma MNMESSAR Unspecified
Primary Malignant Neoplasm, Other, Specify MNOTH Hepatic
Primary Rhabdomyosarcoma MNRHAB Hepatic
PTLD, Monomorphic PTLDM Allograft
PTLD, NOS PTLDNOS Allograft
PTLD, Polymorphic PTLDP Allograft
Obstructive Uropathy 
Obstructive Uropathy OBSTRURO Not Specified
Other 
Acquired Renal Disease ACQRD Not Specified
Acute Pyelonephritis ACUTEPYELO Not Specified
Alport's Syndrome ALPORTS Not Specified
Analgesic Abuse Nephropathy ANALABUSE Not Specified
Anti-Glomerular Basement Membrane (Anti-GBM) Disease ANTIGBM Not Specified
Congenital Absence (Aplasia) APLASIA Not Specified
Atheroembolic Disease ATHEMBOLIC Not Specified
Coagulation Disorder COAGPATHY Not Specified
Collagen-Vascular Disease COLLAGVASC Not Specified
Congenital Dysplasia CONDYSPL Not Specified
Congenital Hypoplasia CONHYPOPL Not Specified
Cortical Necrosis CORTNECRO Not Specified
Cryoglobulinemia CRYGLOBUL Not Specified
Cystinosis CYSTNOSIS Not Specified
Drug Induced Interstitial Nephritis DRUGINDUCE Not Specified
Eagel Barrett Syndrome EAGLEBARR Not Specified
Fabry's Disease FABRYS Not Specified
Goodpasture's Snydrome GOODPASTUR Not Specified
Gout (Urate) Nephropathy GOUT Not Specified
Granulomatous Pyelonephritis GRANULOPYL Not Specified
Hepatorenal Syndrome HEPATOREN Not Specified
Hereditary-Congenital Disorders HEREDCONG Not Specified
Hereditary Nephritis HEREDNEPHR Not Specified
Horseshoe Kidney HORSESHOE Not Specified
Henoch-Schonlein Purpura HSP Not Specified
IgA Nephropathy (Berger's Disease) IGA Not Specified
IgM Nephropathy IGM Not Specified
Infarction INFARCTION Not Specified
Interstitial Nephritis INTERNEPH Not Specified
Juvenile Nephronophthisis JUVNEPHRON Not Specified
K-Light Chain Glomerulosclerosis KLIGHTCHAI Not Specified
Light Chain Nephropathy LIGHTCHAIN Not Specified
Mixed Connective Tissue Disorder MCTD Not Specified
Medullary Cystic Disease MEDCYST Not Specified
Medullary Sponge Kidney Disease MEDSPONGE Not Specified
Multiple Myeloma MMYELOMA Not Specified
Myoglobinuria MYGLOBIN Not Specified
Nephrolithiasis NEPHLITH Not Specified
Non-Amyloid Fibrillary Glomerulopathy NONAMYFG Not Specified
Other, Specify OTHER All
Oxalosis OXALOSIS Not Specified
Polyarteritis POLYART Not Specified
Pre-Eclalmpsia PREECLALMP Not Specified
Prune-Belly Syndrome PRUNEBELLY Not Specified
Bacterial Gram Positive Pyelonephritis PYELO Not Specified
Pyelonephritis PYELON Not Specified
Congenital Reflux Hydronephrosis REFLUX Not Specified
Renal Cell Carcinoma RENALCA Not Specified
Renal Artery Thrombosis RENARTHROM Not Specified
Renal Vein Thrombosis RVT Not Specified
Sarcoidosis SARCOID Not Specified
Schistosomiasis SCHISTOSOM Not Specified
Scleroderma SCLERODERM Not Specified
Sickle Cell Anemia SICKLECELL Not Specified
Sjogren's Syndrome SJOGRENS Not Specified
Lupus Nephritis SLE Not Specified
Systematic Diseases SYSTEMATIC Not Specified
Tumors TUMORS Not Specified
Undetermined UNDETERM Not Specified
Ureteral Reflux URREFLUX Not Specified
Wegener's Granulomatosis WEGENERS Not Specified
PCKD 
Polycystic Kidney Disease PCKD Not Specified
Preservation Injury 
Primary Non-Function (includes poorly functioning graft) PNF Unspecified
Recurrent Disease 
Recurrence of Native Disease DISREC All
Rejection/GVHD 
Graft Versus Host Disease, GVHD GVHD Hepatic
Acute Rejection REJACT Allograft
Chronic Rejection REJCHR Allograft
Humoral Rejection REJHUM Allograft
Rejection, NOS REJNOS Unspecified
Renal Dysplasia 
Renal Dysplasia RDYSPLASIA Not Specified
Submassive/Massive Necrosis 
Drug Induced Fulminant Hepatic Failure, Specifiy AFDRUG Hepatic
AHN, Hepatitis EBV AFEBV Hepatic
AHN, Hepatitis A Virus AFHAV Hepatic
AHN, Hepatitis B + Delta Virus AFHBDV Hepatic
AHN, Hepatitis B Virus AFHBV Hepatic
AHN, Hepatitis E Virus AFHEV Hepatic
AHN, Herpes Simplex Virus, Type I AFHSV1 Hepatic
AHN, Herpes Simplex Virus, Type II AFHSV2 Hepatic
AHN, Herpes Simplex Virus, Unknown AFHSVUNK Hepatic
AHN, Hepatitis Herpes Simplex/Varicella-Zoster AFHSV-VZ Hepatic
Fulminant Hepatic Failure, Other, Specify AFOTH Hepatic
Fulminant Hepatic Failure, Cause Unknown AFUNK Hepatic
AHN, Wilson AFWILSON Hepatic
Toxic 
Non-Alcoholic Steatohepatitis(NASH), Specify CSTEAT Hepatic
TPN-Induced Liver Failure CTPN Hepatic
Alcoholic Cirrhosis Without Alcoholic Hepatitis ETOH Hepatic
Alcoholic Cirrhosis With Alcoholic Hepatitis ETOHEP Hepatic
Trauma/Accident 
Trauma, Other, Specify TRAUMAOTH Not Specified
Unspecified 
SMV Thrombosis I001 Unspecified
SMA Thrombosis I002 Unspecified
Hypercoagulable State I003 Unspecified
Chron's Disease I004 Unspecified
Volvulus I005 Unspecified
Vascular Disorder 
Artery Stricture/Other Problem, Non Technical ASTRICT Hepatic
Budd-Chiari, Myeloproliferative Disease BCMYELO Hepatic
Budd-Chiari, Birth Control Pills BCOC Hepatic
Budd-Chiari, Other, Specify BCOTH Hepatic
Budd-Chiari, Polycythemia Vera BCPCV Hepatic
Budd-Chiari, Unknown BCUNK Hepatic
Hepatic Artery Stricture/Other Problem HAS/O Hepatic
Hepatic Arterial Thrombosis HAT Hepatic
Ischemic Changes, NOS ISCHNOS All
Portal Vein Thrombosis PVT Allograft
Vascular Disorder/Thrombosis, NOS VASCNOS Vascular
Veno-Occlusive Disease VENOCC Unspecified