Description Code
1 Acute Rejection REJACT
2 Adenovirus Infection INADV
3 "AHN, Hepatitis A Virus" AFHAV
4 "AHN, Hepatitis B + Delta Virus" AFHBDV
5 "AHN, Hepatitis B Virus" AFHBV
6 "AHN, Hepatitis E Virus" AFHEV
7 "AHN, Hepatitis EBV" AFEBV
8 "AHN, Hepatitis Herpes Simplex/Varicella-Zoster" AFHSV-VZ
9 "AHN, Herpes Simplex Virus, Type I" AFHSV1
10 "AHN, Herpes Simplex Virus, Type II" AFHSV2
11 "AHN, Herpes Simplex Virus, Unknown" AFHSVUNK
12 "AHN, Wilson" AFWILSON
13 "Alagille Syndrome, Kasai" ALLSYNK
14 "Alagille Syndrome, No Kasai" ALLSYNO
15 "Alagille Syndrome, Unknown" ALLSYNUNK
16 Alcoholic Cirrhosis With Alcoholic Hepatitis ETOHEP
17 Alcoholic Cirrhosis Without Alcoholic Hepatitis ETOH
18 Alpha-1-Antitrypsin Deficiency A1ATD
19 "Amyloidosis, FAP" AMYFAP
20 "Amyloidosis, Other" AMYOTH
21 "Amyloidosis, Primary" AMY1
22 "Amyloidosis, Secondary" AMY2
23 "Amyloidosis, Unknown" AMYUNK
24 Angiosarcoma MNANGIO
25 "Artery Stricture/Other Problem, Non Technical" ASTRICT
26 Autoimmune-Induced Cirrhosis CAHAI
27 Bacterial Sepsis/Ischemia INBACSEP
28 "Benign Neoplasia, Other, Specify" BNOTH
29 "Bile Duct Cancer, With PSC" MNBDCAP
30 "Bile Duct Cancer, Without PSC" MNBDCAO
31 "Biliary Atresia, Unclassified" BAUNK
32 "Biliary Complications, Unspecified" BICOMPUNS
33 "Biliary Hypoplasia, Kasai" BIHYPOK
34 "Biliary Hypoplasia, No Kasai" BIHYPOO
35 "Biliary Hypoplasia, Unknown" BIHYPOUNK
36 "Budd-Chiari, Birth Control Pills" BCOC
37 "Budd-Chiari, Myeloproliferative Disease" BCMYELO
38 "Budd-Chiari, Other, Specify" BCOTH
39 "Budd-Chiari, Polycythemia Vera" BCPCV
40 "Budd-Chiari, Unknown" BCUNK
41 Caroli's Disease CAROLIS
42 Caroli's Syndrome CAROLISYND
43 "Cholangiocarcinoma, NOS" MNCCNOS
44 "Cholangiocarcinoma, With PSC" MNCCP
45 "Cholangiocarcinoma, Without PSC" MNCCO
46 Choledochal Cyst CHOLCYST
47 "Chronic Hepatitis/Cirrhosis, Other, Specify" CAHOTH
48 "Chronic Hepatitis/Cirrhosis, Unknown" CAHUNK
49 Chronic Rejection REJCHR
50 Congenital Hepatic Fibrosis CHF
51 Cryptogenic Cirrhosis CCRYPT
52 Cystic Fibrosis CF
53 "Cytomegalovirus, CMV Infection" INCMV
54 "Drug Induced Fulminant Hepatic Failure, Specifiy" AFDRUG
55 "Drug-Induced Cirrhosis, Specify" CAHDRUG
56 Enterovirus Infection INENV
57 Epithelioid Hemangioendothelioma MNEH
58 Erythrophagocytic Lymphohistiocytosis MMERYLYM
59 "Extra and Intra-Hepatic Biliary Atresia, Kasai" EIBAK
60 "Extra and Intra-Hepatic Biliary Atresia, No Kasai" EIBAO
61 "Extra and Intra-hepatic Biliary Atresia, Unknown" EIBAUNK
62 "Extra-Hepatic Biliary Atresia, Kasai" EXBAK
63 "Extra-Hepatic Biliary Atresia, No Kasai" EXBAO
64 "Extra-Hepatic Biliary Atresia, Unknown" EXBAUNK
65 "Familial Cholestasis, Byler" FCBYLER
66 "Familial Cholestasis, Other" FCOTH
67 "Familial Cholestasis, Summerskill" FCSUMMER
68 Focal Nodular Hyperplasia(s) BNFNH
69 Fructosemia FRUCT
70 "Fulminant Hepatic Failure, Cause Unknown" AFUNK
71 "Fulminant Hepatic Failure, Other, Specify" AFOTH
72 Fungal Sepsis INFUNGSEP
73 Galactosemia GALAC
74 Gaucher's Disease GAUCHER
75 Germ Cell Tumor MMGCT
76 Giant Cell Hepatitis CAHGC
77 "Glycogen Storage Disease, Type I" GSDI
78 "Glycogen Storage Disease, Type IV" GSDIV
79 "Graft Versus Host Disease, GVHD" GVHD
80 HBV+ Delta-Induced Cirrhosis CAHBD
81 HBV-Induced Cirrhosis CAHB
82 HCV-Induced Cirrhosis CAHC
83 Hemangioma BNHEM
84 Hemochromatosis HEMOHO
85 Hepatic Adenoma(s) BNADEN
86 Hepatic Arterial Thrombosis HAT
87 Hepatic Artery Stricture/Other Problem HAS/O
88 Hepatitis B + Delta Virus INHBVD
89 Hepatitis B Virus INHBV
90 Hepatitis C Virus INHCV
91 Hepatoblastoma MNHPBLT
92 "Hepatocellular Carcinoma, Fibrolamellar Variant" MNFLHCC
93 "Hepatocellular Carcinoma, Normal Variant" MNHCC
94 "Herpes Simplex Virus, Type I" INHSV1
95 "Herpes Simplex Virus, Type II" INSHV2
96 "Herpes Simplex Virus, Unknown" INHSVUNK
97 HHV VI Infection INHHVVI
98 HHV VIII Infection INHHVVIII
99 "Human Immunodeficiency Virus, HIV" INHIV
100 Humoral Rejection REJHUM
101 "Hyperlipidemia, Type II" HYLIP
102 Indian Childhood Cirrhosis INDIANCC
103 "Infection, Other, Specify" INFOTH
104 Inflammatory Pseudo-Tumor BNPSEU
105 Influenza INFLUENZA
106 "Intra-Hepatic Biliary Atresia, Kasai" INBAK
107 "Intra-Hepatic Biliary Atresia, No Kasai" INBAO
108 "Intra-Hepatic Biliary Atresia, Unknown" INBAUNK
109 "Ischemic Changes, NOS" ISCHNOS
110 Langerhans Cell Histiocytosis MMLCH
111 Lymphangiomyomatosis BNLYMGIO
112 "Lymphoma, Burkitt" MMLYMBUR
113 "Lymphoma, HD" MMLYMHD
114 "Lymphoma, Other" MMLYMOTH
115 "Malignant Lymphoma, Non-PTLD" MMLYM
116 Mesenchymal Hamartoma BNMESHAM
117 Mesenchymal Sarcoma MNMESSAR
118 "Metabolic Disease, Other, Specify" METOTH
119 Metastatic Carcinoid MMCAR
120 Metastatic Gastrinoma MMGAS
121 Metastatic Glucagonoma MMGLU
122 Metastatic Insulinoma MMINS
123 "Metastatic Malignancy, Other, Specify" MMOTH
124 "Metastatic Neuroendocrine, NOS" MMNEUENNOS
125 Mixed HCC/CC MNCCHCC
126 Neonatal Hemochromatosis NEOHEM
127 "Neonatal Hepatitis, Acute" INNEO
128 "Neonatal Hepatitis, Chronic" CAHNEO
129 Neuroblastoma MMNEURO
130 Neurovisceral Storage Disease NEUVIS
131 Niemann-Pick Disease NIEMPICK
132 "Nodular Regenerative Hyperplasia, NRH" BNNRH
133 "Non-A, Non-B CAH (Pre-1991 Cases)" CAHNANB
134 "Non-Alcoholic Steatohepatitis(NASH), Specify" CSTEAT
135 "Other, Specify" OTHER
136 Papillomavirus INPAPV
137 "Polycystic Disease, NOS" PCDNOS
138 "Polycystic Disease, With Renal Involvment" PCLKD
139 "Polycystic Disease, Without Renal Involvment" PCLD
140 "Porphyria, Protoporphyria" PROTOPHY
141 Portal Vein Thrombosis PVT
142 Primary Biliary Cirrhosis PBC
143 "Primary Malignant Neoplasm, Other, Specify" MNOTH
144 Primary Non-Function (includes poorly functioning graft) PNF
145 Primary Rhabdomyosarcoma MNRHAB
146 "Primary Sclerosing Cholangitis, Crohn's disease" PSCCRH
147 "Primary Sclerosing Cholangitis, No bowel Disease" PSCNO
148 "Primary Sclerosing Cholangitis, Ulcerative Colitis" PSCUC
149 "Primary Sclerosing Cholangitis, Unknown Bowel Disease" PSCUNK
150 Protein C Deficiency METPROC
151 "PTLD, Monomorphic" PTLDM
152 "PTLD, NOS" PTLDNOS
153 "PTLD, Polymorphic" PTLDP
154 Recurrence of Native Disease DISREC
155 Recurrent Malignancy DISRECM
156 "Rejection, NOS" REJNOS
157 Reye's Syndrome REYES
158 "Sclerosing Cholangistis, S/P Langerhans Cell Disease" SCLCD
159 "Secondary Biliary Cirrhosis, Iatrogenic" BC2IAT
160 "Secondary Biliary Cirrhosis, Other, Specify" BC2OTH
161 "Secondary Biliary Cirrhosis, Trauma" BC2TRA
162 Secondary Rhabdomyosarcoma MMRHABDO
163 Smooth Muscle Tumor MMSMT
164 Spindle-Cell Tumor MMSCT
165 Teratoma MMTERAT
166 Toxoplasmosis INTOXO
167 TPN-Induced Liver Failure CTPN
168 Tyrosinemia TYRO
169 Vascular Malformation BNVASMAL
170 Veno-Occlusive Disease VENOCC
171 "Viral Infection, Other, Specify" VIRALOTH
172 Viral Sepsis INVIRALSEP
173 Wilson's Disease WILSON
174 Wolman Disease WOLMAN
175 Zellweger Syndrome ZELLWEGER